Rare case of Congenital Infantile Fibrosarcoma of hand – A case report

Abhinav Sihag, Senthil Ganesh Kamaraj, Sridhar S, Arathi Srinivasan, Seyed Rabia

CHILDS Trust Medical Research Foundation, Kanchi Kamakoti CHILDS Trust Hospital, 12-A Nageswara Road, Nungambakkam, Chennai 600034, India.

Abstract

Congenital infantile fibrosarcoma (CIFS) is a rare paediatric soft tissue tumour that presents most commonly at or after birth within the first year of life. It occurs most frequently over the extremity on the distal segments, followed by head, neck, and trunk. The usual presentation is a painless soft tissue mass with extensive local invasion and rare metastasis. The recommended treatment of CIFS is wide local excision. In recent times, preoperative chemotherapy is found to be useful in unresectable tumors by reducing tumor volume and hence reducing the morbidity of an extensive resection.